WebJuvenile xanthogranuloma (JXG), an ocular masquerade syndrome affecting young children, is a member of the non-Langerhans cell histiocytoses (NLCH). JXG may exceptionally manifest as an intraocular tumor with the iris being the predilection site. WebAug 1, 2024 · In summary, iris JXG can have atypical presentations, simulating diffuse anterior retinoblastoma or tapioca or diffuse iris melanoma. Fluorescein angiography reveals diffuse leakage and AS-OCT can show a generalized epi-iridic membrane in a stalagmite configuration.
Iris juvenile xanthogranuloma in an infant - ResearchGate
WebFeb 22, 2024 · Lisch nodules, traditionally described as iris hamartomas are one of the pathognomic markers of neurofibromatosis type 1 (NF1) and are rarely seen in individuals without NF1 like segmental neurofibromatosis and Watson syndrome. WebMar 1, 2024 · Juvenile xanthogranuloma primarily affects the skin of infants and young children. It infrequently can involve the structures of the eye and orbit and rarely occurs in individuals beyond the second decade of life. We present a case of adult onset xanthogranuloma (AXG) involving the eyelid of a 29-year-old female. high tie for horses
Juvenile xanthogranuloma of the iris in an adult - PubMed
WebOct 26, 2024 · Juvenile xanthogranuloma is a non-Langerhans cell histiocytosis affecting young children. Although primarily a cutaneous disorder, it can affect the eye and its … A diagnosis of JXG is suspected in patients with characteristicyellowish cutaneous lesions. Excisional biopsy can be performed to confirm the diagnosisin cutaneous eyelid or conjunctival lesions. All patients with cutaneous JXGare advised to have a complete ophthalmic examination. In casesof iris JXG, anterior … See more Juvenile xanthogranuloma (JXG) is a rare benign histiocytic proliferation that develops in infants and young children. JXG is the most common form of non-Langerhans’ cell histiocytoses. It is characterized by the … See more For eyelid JXG, excisional biopsy is commonly performed and is both diagnostic and therapeutic. Alternatively, topical and … See more The prognosis for patients with JXG is generally good. The skin lesions usually regress (or at least stabilize) with time, and even large, deeply … See more WebSep 26, 2024 · Juvenile xanthogranuloma (JXG) is a benign, proliferative disorder belonging to the broad group of non-Langerhans cell histiocytoses and is typically a disorder of … how many dry tablespoons in a cup